Información adicional

• Num_publicacion 78(1-2)
• Resumen_ingles

  Introduction: Congenital pulmonary lymphangiectasia is a rare entity characterized by congenital dilatation of pulmonary lymphatics at different levels. Clinically presents with severe respiratory failure refractory to treatment that appears in the first hours of life, with high mortality.

  Case report: We report the case of a term infant with no history of interest, who died suddenly after two hours of life. The autopsy revealed the presence of scattered cystic dilations pulmonary lymphatics, without other associated malformations, establishing primary congenital pulmonary lymphangiectasia as the cause of death.

  Discussion: Congenital pulmonary lymphangiectasia is a rare disease of unknown origin and poorly documented. The primary form, limited to pulmonary lymphatic tissue, prenatal diagnosis is difficult, presents high mortality.

• Palabras_clave_ingles Congenital pulmonary lyphangiectasis lymphatic system perinatal death.
• Todos_autores C.M. González Álvarez, M. García Reymundo
• autores listados C.M. González Álvarez, M. García Reymundo
• Correspondecia

  M. García Reymundo. Servicio de Pediatría. Unidad de Neonatología. Hospital de Mérida. Polígono Nueva Ciudad s/n.
  06800 Mérida (Badajoz). Correo electrónico: mercedes.garciare@salud-juntaex.es

• Titulo_ingles Primary congenital pulmonary lymphangiectasis presenting as sudden newborn
• Centros_trabajo Servicio de Pediatría. Unidad de Neonatología. Hospital de Mérida. Mérida
• Publicado en Acta Pediatr Esp. 2020; 78(1-2): e73-e76
• copyright ©2020 Ediciones Mayo, S.A.
• Tipo de Artículo Clínico (Microdatos) Case Reports